Ann R Coll Surg Engl. Oct;97(7):e doi: /rcsann Doege-Potter Syndrome. Ahluwalia N(1), Attia R(1), Green A(1), Cane P(1). Doege-Potter syndrome presenting with hypoinsulinemic hypoglycemia in a patient with a malignant extrapleural solitary fibrous tumor: a case. We described here a patient with an SFTP with Doege-Potter syndrome who was successfully treated with complete resection. Although lesions.

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Doege—Potter syndrome DPSa paraneoplastic syndrome, presents as a hypoinsulinemic hypoglycemia from the ectopic secretion of insulin-like growth factor II from a solitary fibrous tumor which may be intrapleural or extrapleural in origin.

Doege–Potter Syndrome, cause of nonislet cell tumor hypoglycemia: the first case report from Nepal

Non-islet cell tumor-induced hypoglycemia: Dear Editor, A male, year-old patient admitted because of a progressive increase of the abdominal volume for five months, in association with daily episodes of sudden sweating with syncope. N Engl J Med ; A clinicopathologic review of cases.

A male, year-old patient admitted because of a progressive increase of the abdominal volume for five months, in association with daily episodes of sudden sweating with syncope. Imaging features of solitary fibrous tumors. Morpho-histopathological analysis in syndrkme with the immunohistochemical profile indicated a malignant solitary fibrotic tumor SFT with extensive areas of necrosis.

Physical examination revealed the presence of a palpable mass in the right flank and hypogastrium.

It may cause pain and symptoms resulting from adjacent structures compression 5. Find articles by Leandro Accardo Mattos. Find articles by Marlon Augusto Schiocchet Monarim. The lower portion of the mass is less vascularized. Malignant SFTs are typically large, presenting areas of necrosis and hemorrhage in addition to cellular atypia and a high number of mitotic figures 5. Am J Surg Pathol ; Serum high molecular weight form of insulin-like growth factor II from patients with non-islet cell tumor hypoglycemia is O-glycosylated.


Solitary fibrous tumors of the soft tissues: For permission for commercial use of this work, please see paragraphs 4. This is the first case of solitary fibrous tumor of pleura with DPS reported from Nepal. Br J Cancer ; Axial MRI T1-weighted image with fat saturation after intravenous contrast gadolinium injection in the region of the upper portion of the lesion shows findings similar to the ones observed at CT. No significant change of mixed alveolar and interstitial infiltration over both lung fields compared with last film, more in favor of inflammatory process Click here to view.

Javascript is currently disabled in your browser. How to cite this article: After intravenous contrast injection gadoliniumthe mass exhibited enhancement similar to the one above described for CT. Several features of this site will not function whilst javascript is disabled.

Doege-Potter syndrome | Radiology Reference Article |

J Cardiothorac Surg ;4: Author information Copyright and License information Disclaimer. This work is published and licensed by Dove Medical Press Limited. Histopathological and immunohistochemical analyzes are necessary to confirm the diagnosis 6. You can learn about what data of yours we retain, how it is processed, who it pottre shared with and your right to have your data deleted by reading our Privacy Policy. Calcifications are rarely found 5 – 7.

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Management of non-islet-cell tumor hypoglycemia: Complete tumor resection remained the only definitive treatment. Please review our privacy policy.

The most common location was the pleural cavity left 12 cases and right 28 cases. Support Center Support Center.

Doege–Potter syndrome – Wikipedia

Glucocorticoid therapy doeege hypoglycemia in insulin-like growth factor-II producing solitary fibrous tumor. The patient utilized prednisone for glycemic control and underwent percutaneous biopsy and later surgical intervention. Hypoglycemia mediated by paraneoplastic production of insulin like growth factor-2 from a malignant renal solitary fibrous tumor – clinical case and literature review.

J Med Case Rep. Solitary fibrous tumors of the pleura: SFT is a rare neoplasia and, in spite of its originally described pottet origin, it may occur in any site of the body 5 – 8. Localized benign and malignant fibrous tumors of the pleura.

Since his hospital discharge, the patient has not presented any hypoglycemic episode. Age of onset varied from 24 to 85 years mean 59 yearswith 47 males and 28 females, and gender unavailable for 1 case.